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Japanese Biliary Atresia Registry

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Abstract

The Japanese Biliary Atresia Registry (JBAR) was launched in 1989 by the Japanese Biliary Atresia Society (JBAS). JBAR employed an initial questionnaire, a questionnaire for liver transplantation, and a follow-up questionnaire. The questionnaire has been sent to the pediatric surgeons of JBAS member institutions and the hospitals in which council members of the Japanese Society of Pediatric Surgeons are working. One hundred and twenty-three hospitals have been included in JBAR between 1989 and 2015. Each patient is to be followed up for 30 years. Between 1989 and 2015, 3160 patients have been registered in JBAR. Among them, 1236 patients underwent liver transplantation. Follow-up questionnaire is also going on. 20-year overall and native-liver survival rates were 89 and 49%, respectively. The surgical outcome of BA has markedly improved owing to the co-operation of Kasai portoenterostomy and liver transplantation. Japanese big database of BA is now available.

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References

  1. Japanese Biliary Atresia Society (1992) Japanese Biliary Atresia Registry 1989–1990. J Jpn Soc Pediatr Surg 28:1258–1263 (in Japanese)

    Google Scholar 

  2. Japanese Biliary Atresia Society (1993) Japanese Biliary Atresia Registry 1991. J Jpn Soc Pediatr Surg 29:370–375 (in Japanese)

    Google Scholar 

  3. Japanese Biliary Atresia Society (1994) Japanese Biliary Atresia Registry 1992. J Jpn Soc Pediatr Surg 30:320–326 (in Japanese)

    Google Scholar 

  4. Japanese Biliary Atresia Society (1995) Japanese Biliary Atresia Registry 1993. J Jpn Soc Pediatr Surg 31:264–269 (in Japanese)

    Google Scholar 

  5. Japanese Biliary Atresia Society (1996) Japanese Biliary Atresia Registry 1994. J Jpn Soc Pediatr Surg 32:331–336 (in Japanese)

    Google Scholar 

  6. Japanese Biliary Atresia Society (1997) Japanese Biliary Atresia Registry 1995. J Jpn Soc Pediatr Surg 33:319–324 (in Japanese)

    Google Scholar 

  7. Japanese Biliary Atresia Society (1998) Japanese Biliary Atresia Registry 1996. J Jpn Soc Pediatr Surg 34:349–354 (in Japanese)

    Google Scholar 

  8. Japanese Biliary Atresia Society (1999) Japanese Biliary Atresia Registry 1997. J Jpn Soc Pediatr Surg 35:279–284 (in Japanese)

    Google Scholar 

  9. Japanese Biliary Atresia Society (2000) Japanese Biliary Atresia Registry 1998. J Jpn Soc Pediatr Surg 36:348–353 (in Japanese)

    Google Scholar 

  10. Japanese Biliary Atresia Society (2001) Japanese Biliary Atresia Registry 1999. J Jpn Soc Pediatr Surg 37:327–331 (in Japanese)

    Google Scholar 

  11. Japanese Biliary Atresia Society (2002) Japanese Biliary Atresia Registry 2000. J Jpn Soc Pediatr Surg 38:319–324 (in Japanese)

    Google Scholar 

  12. Japanese Biliary Atresia Society (2003) Japanese Biliary Atresia Registry 2001. J Jpn Soc Pediatr Surg 39:222–227 (in Japanese)

    Google Scholar 

  13. Japanese Biliary Atresia Society (2004) Japanese Biliary Atresia Registry 2002. J Jpn Soc Pediatr Surg 40:209–216 (in Japanese)

    Google Scholar 

  14. Japanese Biliary Atresia Society (2005) Japanese Biliary Atresia Registry 20035. J Jpn Soc Pediatr Surg 41:246–253 (in Japanese)

    Google Scholar 

  15. Japanese Biliary Atresia Society (2006) Japanese Biliary Atresia Registry 2004. J Jpn Soc Pediatr Surg 42:287–294 (in Japanese)

    Google Scholar 

  16. Japanese Biliary Atresia Society (2007) Japanese Biliary Atresia Registry 2005. J Jpn Soc Pediatr Surg 43:175–184 (in Japanese)

    Google Scholar 

  17. Japanese Biliary Atresia Society (2008) Japanese Biliary Atresia Registry 2006. J Jpn Soc Pediatr Surg 44:167–176 (in Japanese)

    Google Scholar 

  18. Japanese Biliary Atresia Society (2009) Japanese Biliary Atresia Registry 2007. J Jpn Soc Pediatr Surg 45:235–245 (in Japanese)

    Google Scholar 

  19. Japanese Biliary Atresia Society (2010) Japanese Biliary Atresia Registry 2008. J Jpn Soc Pediatr Surg 46:284–295 (in Japanese)

    Google Scholar 

  20. Japanese Biliary Atresia Society (2011) Japanese Biliary Atresia Registry 2009. J Jpn Soc Pediatr Surg 47:274–285 (in Japanese)

    Google Scholar 

  21. Japanese Biliary Atresia Society (2012) Japanese Biliary Atresia Registry 2010. J Jpn Soc Pediatr Surg 48:259–269 (in Japanese)

    Google Scholar 

  22. Japanese Biliary Atresia Society (2013) Japanese Biliary Atresia Registry 2011. J Jpn Soc Pediatr Surg 49:277–289 (in Japanese)

    Google Scholar 

  23. Japanese Biliary Atresia Society (2014) Japanese Biliary Atresia Registry 2012. J Jpn Soc Pediatr Surg 50:273–278 (in Japanese)

    Google Scholar 

  24. Japanese Biliary Atresia Society (2015) Japanese Biliary Atresia Registry 2013. J Jpn Soc Pediatr Surg 51:268–274 (in Japanese)

    Google Scholar 

  25. Japanese Biliary Atresia Society (2016) Japanese Biliary Atresia Registry 2014. J Jpn Soc Pediatr Surg 52:291–297 (in Japanese)

    Google Scholar 

  26. Japanese Biliary Atresia Society (2017) Japanese Biliary Atresia Registry 2015. J Jpn Soc Pediatr Surg 53:319–325 (in Japanese)

    Google Scholar 

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Correspondence to Masaki Nio.

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Nio, M. Japanese Biliary Atresia Registry. Pediatr Surg Int 33, 1319–1325 (2017). https://doi.org/10.1007/s00383-017-4160-x

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