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Redo pullthrough for Hirschsprung disease

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Abstract

Pullthrough procedures for Hirschsprung diseases typically have favorable results. However, some children experience long-term postoperative complications comprising stooling disorders, such as intermittent enterocolitis, severe stool retention, intestinal obstruction, as well as incontinence. Reoperative Hirschsprung Disease surgery is complex. This begins with the workup after the initial presentation following primary pullthrough, continues with the definitive surgical correction with redo pullthrough, and ends with long-term follow-up of individuals. The decision tree can be varied with each patient. The operating pediatric surgeon must be able to utilize different operations and treatment options available. While lesser procedures may provide relief in a select population, those with residual aganglionosis or transition zone pathology or mechanical problems will likely require a redo pullthrough. Thus, the diagnostic workup, treatment plan, and definitive surgical care should be coordinated, and executed by an experienced, specialized team at a pediatric referral center.

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Authors and Affiliations

  1. Department of Surgery, Section of Pediatric Surgery, University of Michigan, 1540 East Hospital Drive, Ann Arbor, Michigan, 48109–4211, USA

    Matthew W. Ralls, Arnold G. Coran & Daniel H. Teitelbaum

Authors
  1. Matthew W. Ralls
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  2. Arnold G. Coran
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  3. Daniel H. Teitelbaum
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Correspondence to Arnold G. Coran.

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Ralls, M.W., Coran, A.G. & Teitelbaum, D.H. Redo pullthrough for Hirschsprung disease. Pediatr Surg Int 33, 455–460 (2017). https://doi.org/10.1007/s00383-016-4045-4

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  • DOI: https://doi.org/10.1007/s00383-016-4045-4

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