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Initiation of ECMO for ventilator-dependent respiratory failure in an infant with Pompe’s

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Abstract

We present a 7-month-old male with Pompe’s disease with respiratory failure requiring extracorporeal membrane oxygenation that received enzyme replacement therapy. There are no published cases of the use of extracorporeal membrane oxygenation in a patient with Pompe’s disease, or the use of enzyme replacement therapy in the setting of acute respiratory failure.

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Authors and Affiliations

  1. General Surgery Department, Dwight David Eisenhower Army Medical Center, 300 E Hospital Road, Ft Gordon, Augusta, GA, 30905, USA

    Christina Riojas

  2. Children’s Hospital of Georgia, Augusta, GA, USA

    Walter Pipkin

Authors
  1. Christina Riojas
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  2. Walter Pipkin
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Correspondence to Christina Riojas.

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Riojas, C., Pipkin, W. Initiation of ECMO for ventilator-dependent respiratory failure in an infant with Pompe’s. Pediatr Surg Int 30, 553–555 (2014). https://doi.org/10.1007/s00383-014-3470-5

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  • DOI: https://doi.org/10.1007/s00383-014-3470-5

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