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Pediatric Surgery International

, Volume 29, Issue 7, pp 745–748 | Cite as

Extra-hepatic bile duct hamartoma in a 10-month-old with a morgagni hernia and multiple anatomical anomalies: a rare and incidental finding

  • Adil A. Shah
  • Michael Karass
  • Andrew J. Page
  • Bahig M. ShehataEmail author
  • Megan M. Durham
Case Report
  • 214 Downloads

Abstract

Von Meyenburg complexes (VMCs), also known as bile duct hamartomas, are a part of a group of ductal plate malformations. They are typically present intrahepatically. In this case, we present to our knowledge the first report of an extra-hepatic VMC in the pediatric population. The patient presented as a 10-month-old infant with a weeklong history of progressive breathing difficulty. A chest radiograph was obtained, showing intestinal loops in the thoracic cavity consistent with a Morgagni’s hernia, unrelated to his breathing difficulty. The patient then underwent an elective repair of his congenital diaphragmatic defect. During the operation, the bile duct hamartoma was found adherent to the accessory lobe of the liver, present to the left of the ligamentum teres.

Keywords

Choledochal Cyst Ipratropium Bromide Congenital Diaphragmatic Hernia Ligamentum Teres Ductal Plate 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Adil A. Shah
    • 1
  • Michael Karass
    • 2
  • Andrew J. Page
    • 3
  • Bahig M. Shehata
    • 2
    Email author
  • Megan M. Durham
    • 3
  1. 1.Medical CollegeAga Khan UniversityKarachiPakistan
  2. 2.Department of Pediatric Pathology, Children’s Health Care of AtlantaEmory University School of MedicineAtlantaUSA
  3. 3.Department of Pediatric SurgeryChildren’s Health Care of Atlanta and Emory UniversityAtlantaUSA

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