Abstract
Malrotation and Hirschsprung’s disease (HSD) are rarely reported together. We report our experience with three patients who presented during the neonatal period in whom the association resulted in diagnostic difficulty. In this report, we focus on the clinical presentation, diagnosis and appropriate management.
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References
Stewart DR, Colodny AL, Daggett WC (1976) Malrotation of the bowel in infants and children: a 15 year review. Surgery 79:716–720
Filston HC, Kirks DR (1981) Malrotation—the ubiquitous anomaly. J Pediatr Surg 16:614–620
Spigland N, Brandt ML, Yazbeck S (1990) Malrotation presenting beyond the neonatal period. J Pediatr Surg 25:1139–1142
Spitz L (2003) Malrotation. In: Puri P (ed) Newborn surgery. Arnold, London, pp 435–439
Torres AM (2003) Malrotation. In: Ziegler MM, Azizkhan RG, Weber TR (eds) Operative Pediatric Surgery. McGraw Hill, New York, pp 609–616
de Bruyn R, Hall CM, Spitz L (1982) Hirschsprung’s disease and malrotation of the mid-gut. An uncommon association. Br J Radiol 55:554–557
Tamburrini O, Bartolomeo-De Iuri A, Palescandolo P, Marte A, Amici G (1986) Hirschsprung’s disease and asymptomatic malrotation: a rare association. Pediatr Radiol 16:250–251
Jain SK, Singla SK, Sharma M, Pathania OP, Taneja SB (1989) Hirschsprung’s disease with intestinal malrotation and midgut volvulus: a rare association. Indian J Gastroenterol 8:201
Ko S, Fujii H, Yamamoto K, Sado S, Yamamoto M, Nakano H (1991) Hirschsprung’s disease associated with intestinal malrotation in an adult and a review of literature. Nippon Geka Gakkai Zasshi 92:469–472
Poenaru D, Uroz-Tristan J, Leclerc S, Murphy S, Bensoussan AL (1995) Imperforate anus, malrotation and Hirschsprung’s disease: a rare association. Eur J Pediatr Surg 5:187–189
Das K, Alladi A, Kini U, Babu MK, D’cruz AJ (2001) Hirschsprung’s disease, associated rare congenital anomalies. Indian J Pediatr 68:835–837
Shanske A, Ferreira JC, Leonard JC, Fuller P, Marion RW (2001) Hirschsprung disease in an infant with a contiguous gene syndrome of chromosome 13. Am J Med Genet 102:231–236
Corsois L, Boman F, Sfeir R, Mention K, Michaud L, Poddevin F, Mestdagh P, Gottrand F (2004) Extensive Hirschsprung’s disease associated with intestinal malrotation. Arch Pediatr 11:1205–1208
Clark LA, Oldham KT (2000) Malrotation. In: Ashcraft KW (ed) Pediatric surgery, 3rd edn. WB Saunders, Philadelphia, pp 425–434
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Gabra, H.O.S., Stewart, R.J. & Nour, S. Midgut malrotation and associated Hirschsprung’s disease: a diagnostic dilemma. Pediatr Surg Int 23, 703–705 (2007). https://doi.org/10.1007/s00383-006-1869-3
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DOI: https://doi.org/10.1007/s00383-006-1869-3