Skip to main content
Log in

A case of pancreatoblastoma prenatally diagnosed as intraperitoneal cyst

  • Case Report
  • Published:
Pediatric Surgery International Aims and scope Submit manuscript

Abstract

Pancreatoblastoma in childhood is a very rare malignant tumor, but is considered to have a relatively good prognosis because of its low metastatic potential. We report 1-day-old female infant who was recently found to have an intraabdominal cyst on prenatal ultrasound examination. The tumor was a unilocular, cystic mass without invasion or metastasis to other organs, allowing total resection. It was diagnosed postnatally with pancreatoblastoma.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Fig. 1
Fig. 2
Fig. 3

Similar content being viewed by others

References

  1. Frantz VK (1959) Tumor of the pancreas. In: Atlas of tumor pathology. Armed forces institute of pathology, Washington DC, Section VII, fasc 27 et 28

  2. Horie A, Yano Y, Kotoo Y, Miwa A (1977) Morphogenesis of pancreatoblastoma, infantile carcinoma of the pancreas. Cancer 39:247–254

    Article  PubMed  CAS  Google Scholar 

  3. Endoh K, Uchiyama T, Iida M (1991) Pancreatoblastoma detected before birth. Jpn J Pediatr Oncol 28:422

    Google Scholar 

  4. Drut R, Jones MC (1988) Congenital pancreatoblastoma I. Beckwith-Wiedemann syndrome: en emerging association. Pediatr Pathol 8:331–339

    Article  PubMed  CAS  Google Scholar 

  5. Klimstra DS, Wenig BM, Adair CF, Heffese CS (1995) Pancreatoblastoma, a clinicopathologic study and review of the literature. Am J Surg Pathol 19:1371

    Article  PubMed  CAS  Google Scholar 

  6. Koh TH, Cooper JE, Newman CL, Walker TM, Kiely EM, Hoffmann EB (1986) Pancreatoblastoma in a neonate with Beckwith-Wiedemann syndrome. Eur J Padiatr 145:435–438

    Article  CAS  Google Scholar 

  7. Potts SR, Brown S, Ohara D (1986) Pancreatoblastoma in a neonate associated with Beckwith-Wiedemann syndrome. Z Kinderchir 41:56

    PubMed  CAS  Google Scholar 

  8. Robey G, Daremann A, Martin DJ (1983) Pancreatic carsinoma in a neonate. Pediatr Radiol 13:284

    Article  PubMed  CAS  Google Scholar 

  9. Defachelles AS, Martin de Lassalle E, Bouterd P, Nelken B, Schneider P, Patte C (2001) Pancreatoblastoma in childhood: clinical course and therapeutic management of seven patients. Med Pediatr Oncol 37:47–52

    Article  PubMed  CAS  Google Scholar 

  10. Horie A (1982) Pancreatoblastoma, Histopathologic criteria based upon a review of six cases. In: Humphry GB, Grindey GB, Dehner LP et al. (eds) Pancreatic tumors in children. Martinus Nijhoff Publishers, Hague, pp 159–166

  11. Fonkalsrud EW, Wilkerson JA, Longmire WP (1966) Pancreatoduodenectomy for islet-cell tumor of the pancreas in infancy and childhood. JAMA 197:586–588

    Article  PubMed  CAS  Google Scholar 

  12. Comprodon R, Quintanilla E (1984) Successful long-term result with resection of pancreatic carcinoma in children: favorable prognosis of an uncommon-neoplasm. Surgery 95:420–426

    Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Michihiro Sugai.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Sugai, M., Kimura, N., Umehara, M. et al. A case of pancreatoblastoma prenatally diagnosed as intraperitoneal cyst. Pediatr Surg Int 22, 845–847 (2006). https://doi.org/10.1007/s00383-006-1733-5

Download citation

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00383-006-1733-5

Keywords

Navigation