Abstract
We report a case of right pulmonary agenesis with worsening of mediastinal shift during a viral bronchiolitis at the age of 5 months. The respiratory failure was due to stretching and narrowing of the remaining bronchus, as in postpneumonectomy syndrome. Weaning of respiratory assistance was possible after inserting a tissue expander in the empty side of the thoracic cavity. The correction of the shift brought a liberation of the left main stem bronchus. The main risk is heart compression. The child is now 3 years old and is at home. Filling of the prosthesis is done according to the clinical evolution.
References
Podevin G, Larroquet M, Camby C, Audry G, Plattner V, Heloury Y (2001) Postpneumonectomy syndrome in children: advantages and long-term follow-up of expandable prosthesis. J Pediatr Surg 36:1425–1427
Bittigau K, Bohm J, Kursawe R, Nowotny T, Bittigau P, Konertz W (1995) Pulmonary agenesis in a newborn: implantation of tissue expander to prevent a mediastinal shift. Thorac Cardiovasc Surg 43:287–289
Kosloske AM, Williamson SL (1992) An expandable prosthesis for stabilization of the infant mediastinum following pneumonectomy. J Pediatr Surg 27:1521–1522
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Dobremez, E., Fayon, M. & Vergnes, P. Right pulmonary agenesis associated with remaining bronchus stenosis, an equivalent of postpneumonectomy syndrome. Treatment by insertion of tissue expander in the thoracic cavity. Ped Surgery Int 21, 121–122 (2005). https://doi.org/10.1007/s00383-004-1362-9
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DOI: https://doi.org/10.1007/s00383-004-1362-9