Abstract
An unusual association of esophageal atresia (EA) and tracheoesophageal fistula (TEF) with left amastia and multiple congenital anomalies is presented because of its rarity and successful management. The other associated congenital anomalies included a high variety of anorectal malformation (high-ARM), hypospadias and absent left pectoral muscles with weak shoulder girdle. This case was successfully managed by multi-staged operations to tackle the various associated congenital anomalies. Such a rare association has not been reported previously in the literature.
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References
Bankier A, Brady J, Myers NA (1991) Epidemiology and genetics. In: Beasly SW, Myers NA, Auldist AW (eds) Esophageal atresia. Chapman & Hall Medical, London, pp 19
Baumann W, Greinacher I, Emmrich P, Spranger J (1976) Vater oder Vacterl syndrome. Klin Padiatr 188:328–327
Beasley SW et al. (1992) Urinary tract abnormalities in association with EA frequency, significance and influence on management. Pediatr Surg Int 7:94
Chittmittrapap S, Spitz L, Kiely EM, Brereton RJ (1989) Oesophageal atresia and associated anomalies. Arch Dis Child 64:364–368
Cord-Udy CL, Wright VM, Drake DP (1996) Association of ambiguous genitalia with VATER anomalies and its significance in management. Pediatr Surg Int 11:50
David TJ, O’Callaghan SE (1974) Cardiovascular malformations and esophageal atresia. Br Heart J 36:599
Ein SH, Shandling B, Wessen D, Filler RM (1989) Esophageal atresia with distal tracheoesophageal fistula: associated anomalies and prognosis in 1980s. J Pediatr Surg 24:1055–1059
German JCC, Mahour GH, Woolley MM (1976) Esophageal atresia and associated anomalies. J Pediatr Surg 11:299
Harris J, Kallen B, Robert E (1995) Descriptive epidemiology of alimentary tract atresia. Teratology 52:15–29
Holder TM, Ashcraft KW, Sharp RJ, Amoury RA (1987) Care of infants with esophageal atresia, tracheoesophageal fistula and associated anomalies. J Thorac Cardiovasc Surg 94:828–835
Kluth D (1976) Atlas of esophageal atresia. J Pediatr Surg 11:909–919
Kutiyanawala M, Wyse RK, Brereton RJ, Spitz L, Kiely EM, Drake D, Blake K (1992) CHARGE and esophageal atresia. J Pediatr Surg 27:558–560
Myers NA (1974) Esophageal atresia: the epitome of modern surgery. Ann R Coll Surg Engl 54:277–287
Quan L, Smith DW (1973) The VATER association. J Pediatr 82:104
Spitz L, Kiely EM, Brereton RJ, Drake D (1993) Management of esophageal atresia. World J Surg 17:296–300
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Kumar, V., Apte, A.V., Gangopadhyay, A.N. et al. Tracheoesophageal fistula and amastia with other anomalies: an unusual association. Ped Surgery Int 20, 378–379 (2004). https://doi.org/10.1007/s00383-004-1201-z
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DOI: https://doi.org/10.1007/s00383-004-1201-z