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Appendico-cutaneous fistula in cystic fibrosis

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Abstract

Appendico-cutaneous fistulae are rare. We describe a 12-year-old girl with cystic fibrosis (CF) and a chronically draining sinus in the right iliac fossa, found to be a primary appendico-cutaneous fistula. Misdiagnosis of right iliac fossa pain in patients with CF and the preponderance of complicated disease frequently lead to manifestations of appendicitis rarely seen in usual clinical practice.

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References

  1. Hillyard S (2001) Cystic fibrosis. Genetically programmed to self-destruct. Lancet 358 [Suppl]:S20

  2. Dodge JA, Morison S, Lewis PA, Coles EC, Geddes D, Russell G, Littlewood JM, Scott MT (1997) Incidence, population, and survival of cystic fibrosis in the UK, 1968–95. UK Cystic Fibrosis Survey Management Committee. Arch Dis Child 77:493–496

    CAS  PubMed  Google Scholar 

  3. Littlewood JM (1992) Gastrointestinal complications in cystic fibrosis. J R Soc Med 85 [Suppl 19]:13–19

    Google Scholar 

  4. Dalzell AM, Heaf DP, Carty H (1990) Pathology mimicking distal intestinal obstruction syndrome in cystic fibrosis. Arch Dis Child 65:540–541

    CAS  PubMed  Google Scholar 

  5. Smith HL, Weller PH, Gornall P, Chapman S, Jones TJ (1989) Pitfalls in the diagnosis of appendix abscess in cystic fibrosis. J R Soc Med 82 [Supp1 16]:54–56

    Google Scholar 

  6. Weller PH, Williams J (1986) Clinical features, pathogenesis and management of meconium ileus equivalent. J R Soc Med 79 [Suppl 12]:36–37

  7. Allen ED, Pfaff JK, Taussig LM, McCoy KS (1992) The clinical spectrum of chronic appendiceal abscess in cystic fibrosis. Am J Dis Child 146:1190–1193

    CAS  PubMed  Google Scholar 

  8. Coughlin JP, Gauderer MWL, Stern RC, Doershuk CF, Izant RJ, Zollinger RM Jr (1990) The spectrum of appendiceal disease in cystic fibrosis. J Ped Surg 25:835–839

    CAS  Google Scholar 

  9. Shields MD, Levison H, Reisman JJ, Durie PR, Canny GJ (1991) Appendicitis in cystic fibrosis. Arch Dis Child 66:307–310

    CAS  PubMed  Google Scholar 

  10. Korner H, Sondenaa K, Soreide JA, Andersen E, Nysted A, Lende TH, Kjellevold KH (1997) Incidence of acute nonperforated and perforated appendicitis: age-specific and sex-specific analysis. World J Surg 21:313–317

    Article  CAS  PubMed  Google Scholar 

  11. Cakmak MA, Aaronson IA (1997) Appendicovesical fistula in a girl with cystic fibrosis. J Ped Surg 32:1793–1794

    CAS  Google Scholar 

  12. McCarthy VP, Mischler EH, Hubbard VS, Chernick MS, di Sant Agnese PA (1984) Appendiceal abscess in cystic fibrosis: a diagnostic challenge. Gastroenterology 86:564–568

    CAS  PubMed  Google Scholar 

  13. Schier F (2000) Appendico-ileal fistula in cystic fibrosis. J Ped Surg 35:634–635

    Article  CAS  Google Scholar 

  14. Andersson R, Hugander A, Thulin A, Nystrom PO, Olaison G (1994) Indications for operation in suspected appendicitis and incidence of perforation. BMJ 308:107–110

    CAS  PubMed  Google Scholar 

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Correspondence to Graeme J. Pitcher.

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Rogers, T.N., Joseph, C., Bowley, D.M.G. et al. Appendico-cutaneous fistula in cystic fibrosis. Ped Surgery Int 20, 151–152 (2004). https://doi.org/10.1007/s00383-003-1109-z

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  • DOI: https://doi.org/10.1007/s00383-003-1109-z

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