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A surgical case of pediatric spinal medulloepithelioma

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Abstract

Embryonal tumor with multilayered rosettes (ETMR), C19MC-altered was introduced to the World Health Organization classification of central nervous system tumors in 2016. It is characterized by amplification or fusion of the chromosome 19 microRNA cluster (C19MC) locus at 19q13.42. Medulloepithelioma also an ETMR but lacks C19MC alteration. We report a rare case of spinal medulloepithelioma in a 2-year-old boy and review the literature.

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Acknowledgements

The authors thank Enago (https://www.enago.jp/) for the English language review.

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Authors and Affiliations

  1. Department of Neurosurgery, Faculty of Medicine, Yamagata University, Yamagata-City, Japan

    Kazuki Nakamura, Ken-ichiro Matsuda & Yukihiko Sonoda

  2. Department of Pathological Diagnostics, Faculty of Medicine, Yamagata University, Yamagata-City, Japan

    Takanobu Kabasawa

  3. Department of Pediatrics, Faculty of Medicine, Yamagata University, Yamagata-City, Japan

    Toru Meguro

  4. Department of Anatomic Pathology, Hirosaki University Graduate School of Medicine, Hirosaki, Japan

    Akira Kurose

Authors
  1. Kazuki Nakamura
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  2. Ken-ichiro Matsuda
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  3. Takanobu Kabasawa
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  4. Toru Meguro
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  5. Akira Kurose
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  6. Yukihiko Sonoda
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Correspondence to Yukihiko Sonoda.

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Nakamura, K., Matsuda, Ki., Kabasawa, T. et al. A surgical case of pediatric spinal medulloepithelioma. Childs Nerv Syst 38, 473–477 (2022). https://doi.org/10.1007/s00381-021-05293-7

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  • DOI: https://doi.org/10.1007/s00381-021-05293-7

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