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Limited dorsal myeloschisis with no extradural stalk linking to a flat skin lesion: a case report

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Abstract

Background

Limited dorsal myeloschisis (LDM) is characterized by a fibroneural stalk linking the skin lesion to the underlying spinal cord.

Case presentation 

A 7-month-old girl with a lumbosacral “cigarette-burn” flat skin lesion underwent untethering surgery. The intradural tethering stalk appeared to originate at the dural wall and join the cord with no extradural stalk linking to the skin lesion. Histological examination of the intradural stalk revealed glial fibrillary acidic protein-immunopositive neuroglial tissues in the fibrocollagenous band, which is the central histopathological feature of an LDM stalk.

Conclusion

It is conceivable that the LDM stalk in our patient was originally linked to the skin lesion and subsequently regressed and was replaced by mature adipose tissue. We should be mindful of possible variations in the morphological features of LDM.

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Acknowledgments

We thank Jane Charbonneau, DVM, from Edanz Group (www.edanzediting.com/ac) for editing a draft of this manuscript.

Funding

This work was partly supported by the Research Foundation of Fukuoka Children’s Hospital.

Author information

Authors and Affiliations

  1. Department of Pediatric Neurology, Fukuoka Children’s Hospital, Fukuoka, Japan

    Akiko Hiraoka

  2. Department of Neurosurgery, Fukuoka Children’s Hospital, 5-1-1 Kashii-teriha, Higashi-ku, Fukuoka, 813-0017, Japan

    Takato Morioka & Nobuya Murakami

  3. Department of Neuropathology, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan

    Satoshi O. Suzuki

  4. Department of Neurosurgery, Kitakyushu Municipal Medical Center, Kitakyushu, Japan

    Masahiro Mizoguchi

Authors
  1. Akiko Hiraoka
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  2. Takato Morioka
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  3. Nobuya Murakami
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  4. Satoshi O. Suzuki
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  5. Masahiro Mizoguchi
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Corresponding author

Correspondence to Takato Morioka.

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The authors declare that they have no conflict of interest.

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Hiraoka, A., Morioka, T., Murakami, N. et al. Limited dorsal myeloschisis with no extradural stalk linking to a flat skin lesion: a case report. Childs Nerv Syst 34, 2497–2501 (2018). https://doi.org/10.1007/s00381-018-3938-z

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  • DOI: https://doi.org/10.1007/s00381-018-3938-z

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