Abstract
Background
Lipomyelomeningocele (LMMC) is defined by a low-lying tethered spinal cord protruding posteriorly from the spinal canal and terminating in a lipomatous mass in the subcutaneous meningeal sac. The coexistence of LMMC with split cord malformation (SCM) is rare.
Clinical presentation
We report on a patient with laterally protruded LMMC arising from the hemicord of SCM type I. Direct coronal and axial views (instead of sagittal views) of 3D heavily T2-weighted MR imaging (3D–hT2WI) clearly demonstrated the topographical relationship between both of the hemicords, the bony septum, and nerve roots in the right subcutaneous meningeal sac.
Conclusion
Combined use of axial and coronal images of 3D–hT2W is useful for visualization and surgery of such a complicated anomaly.
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Murakami, N., Morioka, T., Ichiyama, M. et al. Lateral lipomyelomeningocele of the hemicord with split cord malformation type I revealed by 3D heavily T2-weighted MR imaging. Childs Nerv Syst 33, 993–997 (2017). https://doi.org/10.1007/s00381-017-3350-0
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DOI: https://doi.org/10.1007/s00381-017-3350-0