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Primary sporadic Burkitt lymphoma of the orbit, clinical characteristics, management, and outcomes: a case study

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Abstract

Background

Involvement of the orbit with Burkitt’s lymphoma is a very rare presentation of extra-nodal lymphoma.

Illustrative case

We report a case of a 2-year-old female presented an unusual location of sporadic Burkitt’s lymphoma arising in the orbital region. Diagnostic magnetic resonance imagining identified an oval-shaped mass on the lateral rectus of the right orbit that caused dislocation of eyeball, for which she underwent a biopsy from the periorbital swellings.

The mass was histologically confirmed as Burkitt’s lymphoma, and postoperative aggressive chemotherapy was initiated.

We describe clinical diagnosis, histological aspects, radiological features, and current management of this rapidly growing malignant tumor.

Conclusion

Because of the rapid progression of Burkitt lymphoma, and considering that it responds well to treatment, early recognition and appropriate management are important factors for survival and to preserve visual function.

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Authors and Affiliations

  1. Department of neurosurgery, National Institute of Neurology “Mongi Ben Hmida” of Tunis, Faculty of Medicine, University of Tunis el MANAR, Tunis, Tunisia

    Sofiene Bouali, Imed Ben Said, Mohamed Dahmani Yedeas, Khansa Abderrahmen, Nidhal Maatar, Adnen Boubaker, Jalel Kallel & Hafedh Jemel

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  1. Sofiene Bouali
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  2. Imed Ben Said
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  3. Mohamed Dahmani Yedeas
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  4. Khansa Abderrahmen
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  5. Nidhal Maatar
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  6. Adnen Boubaker
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  7. Jalel Kallel
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  8. Hafedh Jemel
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Correspondence to Sofiene Bouali.

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Bouali, S., Said, I.B., Yedeas, M.D. et al. Primary sporadic Burkitt lymphoma of the orbit, clinical characteristics, management, and outcomes: a case study. Childs Nerv Syst 32, 437–440 (2016). https://doi.org/10.1007/s00381-016-3018-1

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  • DOI: https://doi.org/10.1007/s00381-016-3018-1

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