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The nature of double concomitant myxopapillary ependymoma: report of a case

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Abstract

Myxopapillary ependymomas are almost exclusively seen at the conus medullaris/filum terminale/cauda equina region, usually as solitary space-occupying lesions. The authors report the case of a 14-year-old boy with double concomitant myxopapillary ependymoma, proximal and caudal on the filum terminale in which a totally gross removal was achieved in two stages. This presentation is rare and, so far, we have known just three similar cases that were previously reported in children. The true nature of these lesions is controversial, and while some argue that they are related to metastatic seeding, others consider them independent lesions developing synchronously. A review on dissemination of spinal myxopapillary ependymomas was done.

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Authors and Affiliations

  1. Section of Pediatric Neurosurgery, Department of Pediatric Surgery, Fernandes Figueira National Institute for Health of Woman, Child and Adolescent, Oswaldo Cruz Foundation (IFF-Fiocruz), Av. Rui Barbosa, 716, 22250-020, Rio de Janeiro, Brazil

    J. Francisco Salomão, Antonio Rosa Bellas & Tatiana Protzenko Cervante

  2. Department of Pathology, Fernandes Figueira National Institute for Health of Woman, Child and Adolescent, Oswaldo Cruz Foundation (IFF-Fiocruz), Av. Rui Barbosa, 716, 22250-020, Rio de Janeiro, Brazil

    Cecília Vianna de Andrade

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  1. J. Francisco Salomão
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  2. Cecília Vianna de Andrade
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  3. Antonio Rosa Bellas
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  4. Tatiana Protzenko Cervante
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Correspondence to J. Francisco Salomão.

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Salomão, J.F., de Andrade, C.V., Bellas, A.R. et al. The nature of double concomitant myxopapillary ependymoma: report of a case. Childs Nerv Syst 30, 527–530 (2014). https://doi.org/10.1007/s00381-013-2251-0

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  • DOI: https://doi.org/10.1007/s00381-013-2251-0

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