Abstract
Multisutural craniosynostosis as seen in Crouzon’s syndrome can result in raised intracranial pressure, Chiari malformation (CM) and syringomyelia. Posterior calvarial distraction (PD) is a technique for addressing cranio-cephalic disproportion, and this case report describes the reversal of both CM and syrinx in a 6-year-old child who underwent PD initially for raise intracranial pressure.
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Ahmad, F., Evans, M., White, N. et al. Amelioration of Chiari type 1 malformation and syringomyelia following posterior calvarial distraction in Crouzon’s syndrome—a case report. Childs Nerv Syst 30, 177–179 (2014). https://doi.org/10.1007/s00381-013-2202-9
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DOI: https://doi.org/10.1007/s00381-013-2202-9