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Ehlers–Danlos syndrome and neurological features: a review

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Abstract

Ehlers–Danlos Syndrome is a term that comprises a variety of inherited connective tissue disorders characterized primarily by skin hyperextensibility, joints hypermobility and excessive dislocations, easy bruisability, generalized fragility. If much is known about orthopedic or physiatric features of this syndrome, poor is known about the neurological ones. Thus neurological assessment is very important due to the possible various clinical manifestations in this syndrome.

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Authors and Affiliations

  1. Department of Pediatrics, Fondazione IRCCS Policlinico San Matteo, P.le Golgi, 2, 27100, Pavia, Italy

    Salvatore Savasta, Pietro Merli, Lucia Bianchi & Maria Valentina Spartà

  2. Institute of Neurological Science, National Research Council, Catania, Italy

    Martino Ruggieri

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  1. Salvatore Savasta
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Correspondence to Salvatore Savasta.

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Savasta, S., Merli, P., Ruggieri, M. et al. Ehlers–Danlos syndrome and neurological features: a review. Childs Nerv Syst 27, 365–371 (2011). https://doi.org/10.1007/s00381-010-1256-1

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