Abstract
Introduction
Cranial expansion has been the mainstay of initial management of children with Apert syndrome. Surgical timing is a balance between the risk of relapse if performed too early and the possibility of raised intracranial pressure and ossification defects if performed later. Primary occipital expansion has been proposed as a method to delay the timing of frontal surgery. We have applied the principal of spring expansion of patent sutures to expand the posterior cranial fossa without a cranial osteotomy.
Patients and methods
All new Apert syndrome patients seen during the 3-year period December 2004–December 2007 underwent initial occipital expansion without osteotomy using spring expansion of the patent lambdoid suture.
Results
Four new Apert syndrome patients underwent posterior spring expansion of the patent lambdoid suture. Good occipital expansion was achieved in all cases. Standard frontal advancement was performed 5–18 months later. No relapse after frontal advancement has been seen after mean follow-up of 41 months.
Conclusions
Spring expansion of the patent lambdoid suture is an alternative technique to expand the posterior cranial fossa. Compared to current techniques it has very low morbidity. Occipital expansion is thought to treat several of the mechanisms responsible for raised intracranial pressure in Apert syndrome. When performed at 6Â months of age it has enabled us to delay the time at which we would normally perform frontal advancement surgery until a time when the surgical result is likely to be more stable.
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Acknowledgments
Charles Davis learned the spring principles from Professor Claes Lauritzen during a Craniofacial Fellowship in Sweden in 2003/2004.
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The authors of this manuscript have no financial interest in the technology or techniques used in this paper.
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Davis, C., MacFarlane, M.R. & Wickremesekera, A. Occipital expansion without osteotomies in Apert syndrome. Childs Nerv Syst 26, 1543–1548 (2010). https://doi.org/10.1007/s00381-010-1144-8
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DOI: https://doi.org/10.1007/s00381-010-1144-8