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Spontaneous regression of a terminal myelocystocele and associated syringomyelia: a case report

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Abstract

Introduction

Terminal myelocystocele is a rare form of spinal dysraphism characterised by cystic dilatation of the central canal of a low-lying terminal cord. Typical presentation is a skin-covered dorsal mass; early surgical repair has been recommended.

Case report

We present the case of a 4-year-old girl with a terminal myelocystocele and syrinx, which were both observed to spontaneously regress on subsequent magnetic resonance imaging.

Conclusion

Terminal myelocystocele and its associated syrinx may resolve spontaneously. Early surgical repair may not always be necessary.

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Acknowledgements

We thank Dr. Katherine Foster for her assistance with the MR imaging.

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Authors and Affiliations

  1. School of Medicine, Birmingham University, Vincent Drive, Birmingham, B15 2TT, UK

    Andrew J. Durnford

  2. Department of Paediatrics, Birmingham Heartlands Hospital, Bordesley Green East, Birmingham, B9 5SS, UK

    Roopa Mulik

  3. Department of Paediatric Neurosurgery, Birmingham Children’s Hospital, Steelhouse Lane, Birmingham, B4 6NH, UK

    Andrew D. Kay

Authors
  1. Andrew J. Durnford
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  2. Roopa Mulik
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  3. Andrew D. Kay
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Correspondence to Andrew D. Kay.

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Durnford, A.J., Mulik, R. & Kay, A.D. Spontaneous regression of a terminal myelocystocele and associated syringomyelia: a case report. Childs Nerv Syst 26, 403–406 (2010). https://doi.org/10.1007/s00381-009-1065-6

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  • DOI: https://doi.org/10.1007/s00381-009-1065-6

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