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Finding on brain MRI mimicking focal cortical dysplasia in early Rasmussen's encephalitis: a case report and review

Child's Nervous System volume 25, pages 1501–1506 (2009)Cite this article

Abstract

Introduction

Rasmussen's encephalitis (RE) is one of the important causes of refractory seizure. The most impressive clinical manifestation of RE is epilepsia partialis continua (EPC). Others include progressive hemiparesis and neuropsychological deterioration. Currently, the best approach to RE is hemispherectomy.

Case histories

We describe a patient whose clinical manifestations were compatible with RE; however, the initial brain MRI was interpreted as focal cortical dysplasia over right parietal region.

Discussion

The follow-up brain MRI 1 year later showed diffuse atrophy of the brain with more atrophic change in right hemisphere, and the EPC disappeared after right hemispherectomy.

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Conflict of interest

The authors declare that they have no conflict of interest.

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Authors and Affiliations

  1. Department of Pediatrics, Taipei Veterans General Hospital, No. 201, Sec 2, Shih-Pai Road, Taipei, 112, Taiwan

    Kuo-Liang Chiang, Ting-Rong Hsu, Chung-Hao Wang & Kai-Ping Chang

  2. Department of Neurosurgery, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan

    Tai-Tong Wong

  3. Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan

    Shan-Young Kwan

  4. Departments of Pediatrics, Kuang-Tien General Hospital, Taichung, Taiwan

    Kuo-Liang Chiang

  5. National Yang-Ming University School of Medicine, Taipei, Taiwan

    Tai-Tong Wong, Ting-Rong Hsu & Kai-Ping Chang

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  1. Kuo-Liang Chiang
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  2. Tai-Tong Wong
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Correspondence to Kai-Ping Chang.

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Chiang, KL., Wong, TT., Kwan, SY. et al. Finding on brain MRI mimicking focal cortical dysplasia in early Rasmussen's encephalitis: a case report and review. Childs Nerv Syst 25, 1501–1506 (2009). https://doi.org/10.1007/s00381-009-0905-8

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  • DOI: https://doi.org/10.1007/s00381-009-0905-8

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