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Pansynostosis: a review

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Abstract

Introduction

Although rare, pansynostoses are seen and treated by the craniofacial surgeon. To date, a single source that reviews these more severe forms of craniosynostosis is lacking in the literature.

Materials and methods

The present paper outlines and reviews the associations of both syndromic and nonsyndromic cases, potential mechanisms, and the anatomy involved with such forms of premature fusion of the cranial sutures.

Results

Pansynostosis is seen in a myriad of syndromes but can also be identified in nonsyndromic cases. Raised intracranial pressure is a concern in these patients.

Conclusions

Early recognition and treatment of patients with pansynostosis of the cranial sutures is important.

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Authors and Affiliations

  1. Division of Neurosurgery, University of Alabama at Birmingham, Birmingham, AL, USA

    Jeffrey P. Blount, Robert G. Louis Jr. & R. Shane Tubbs

  2. Division of Plastic Surgery, University of Alabama at Birmingham, Birmingham, AL, USA

    John H. Grant

  3. Pediatric Neurosurgery, Children’s Hospital, 1600 7th Avenue South ACC 400, Birmingham, AL, 35233, USA

    R. Shane Tubbs

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  1. Jeffrey P. Blount
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  2. Robert G. Louis Jr.
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Correspondence to R. Shane Tubbs.

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Blount, J.P., Louis, R.G., Tubbs, R.S. et al. Pansynostosis: a review. Childs Nerv Syst 23, 1103–1109 (2007). https://doi.org/10.1007/s00381-007-0362-1

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  • DOI: https://doi.org/10.1007/s00381-007-0362-1

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