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Intraventricular neurocytoma with massive brain stem involvement in a 5-year-old child

Child's Nervous System volume 22, pages 95–98 (2006)Cite this article

Abstract

Introduction

Central neurocytoma is a tumor of neuronal origin that should be taken into consideration in the differential diagnosis of intraventricular neoplasms. Reports of neurocytomas with an extraventricular localization are rare: to our knowledge, the case described here is the first in which a neurocytoma developed within the ventricles but also invaded the brain stem.

Case report

The authors describe the unusual case of a 5-year-old boy with an intraventricular neurocytoma presenting with massive involvement of the basal nuclei and the brain stem. The patient underwent first biopsy and then surgery for ventricular-peritoneal shunting and partial removal of the tumor. Histology showed the tumor to be a typical neurocytoma with Mib-1 <2%. The postoperative course was uneventful. At 3 years’ follow-up, the patient’s clinical condition is stable and there are no signs of disease progression.

Discussion

The literature is reviewed and the characteristics of this unusual tumor are discussed.

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Fig. 1

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Author information

Affiliations

  1. Department of Neurosurgery, University La Sapienza, Rome, Italy

    Jacopo Lenzi, Antonino Raco, Angelo Pichierri & Roberto Delfini

  2. Via dei Fienili 58a, 00186, Rome, Italy

    Jacopo Lenzi

  3. Department of Neurosurgery, INM Neuromed IRCCs, Pozzilli (IS), Italy

    Maurizio Salvati, Alessandro Frati & Felice Giangaspero

Authors
  1. Jacopo Lenzi
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  2. Maurizio Salvati
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  3. Alessandro Frati
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  4. Antonino Raco
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  5. Angelo Pichierri
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  6. Felice Giangaspero
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  7. Roberto Delfini
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Correspondence to Jacopo Lenzi.

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Lenzi, J., Salvati, M., Frati, A. et al. Intraventricular neurocytoma with massive brain stem involvement in a 5-year-old child. Childs Nerv Syst 22, 95–98 (2006). https://doi.org/10.1007/s00381-004-1092-2

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  • DOI: https://doi.org/10.1007/s00381-004-1092-2

Keywords

  • Neurocytoma
  • Pediatric
  • Extraventricular involvement