Abstract
Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.
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Kramer, U., Dörnberger, V., Fenchel, M. et al. Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging. Eur Radiol 13 (Suppl 6), L147–L150 (2003). https://doi.org/10.1007/s00330-003-2061-y
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DOI: https://doi.org/10.1007/s00330-003-2061-y