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Primary hypertrophic osteoarthropathy

Abstract

Pachydermoperiostosis PDP (idiopathic or primary hypertrophic osteoarthropathy) is a rare congenital disease that inherited in an autosomal fashion. The disease is more common in males and develops gradually from adulthood. The disease is characterized by coarse facial features, clubbing of the fingers and radiographic periostitis of the distal long bones. The patient was a 37-year-old man with acroosteolysis and digital clubbing of hands and feet fingers and lion facies.

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Correspondence to Hadi Poormoghim.

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Poormoghim, H., Hosseynian, A. & Javadi, A. Primary hypertrophic osteoarthropathy. Rheumatol Int 32, 607–610 (2012). https://doi.org/10.1007/s00296-010-1667-z

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Keywords

  • Pachydermoperiostosis
  • Primary hypertrophic osteoarthropathy
  • Digital clubbing
  • Acroosteolysis