Abstract
Adult onset Still’s disease (AOSD) is a systemic inflammatory disease characterized by high-fevers, articular involvement, maculopapular rash, hepatosplenomegaly, lymphadenopathy, and a neutrophilic leukocytosis. Though systemic complications of AOSD or its treatment are well described in the literature, CNS involvement in AOSD is exceedingly rare and can have protean manifestations. We present a patient with AOSD who developed chronic meningitis and sensorineural hearing loss on treatment, with a review of prior reported cases of aseptic meningitis, to highlight this rare complication of this uncommon illness.
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Akkara Veetil, B.M., Yee, A.H., Warrington, K.J. et al. Aseptic meningitis in adult onset Still’s disease. Rheumatol Int 32, 4031–4034 (2012). https://doi.org/10.1007/s00296-010-1529-8
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DOI: https://doi.org/10.1007/s00296-010-1529-8