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Hemophagocytic syndrome in adult-onset Still’s disease (AOSD): A must for biologics?—Case report and brief review of the literature

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Abstract

A case of adult-onset Still’s disease complicated by hemophagocytic lymphohistiocytosis is reported. Its management is being discussed on the background of the latest literature with special regard on the use of high-dose corticosteroids and immunosuppressive agents.

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Authors and Affiliations

  1. Department of Medicine, Kantonsspital Aarau, Aarau, Switzerland

    Urs Bürgi

  2. Department of Laboratory Medicine, Kantonsspital Aarau, Aarau, Switzerland

    Adriana Mendez

  3. Department of Rheumatology, Kantonsspital Aarau, Aarau, Switzerland

    Paul Hasler

  4. Department of Rheumatology, Bethesda-Spital Basel, Gellertstrasse 144, CH-4020, Basel, Switzerland

    Hans Dieter Hüllstrung

Authors
  1. Urs Bürgi
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  2. Adriana Mendez
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  3. Paul Hasler
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  4. Hans Dieter Hüllstrung
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Corresponding author

Correspondence to Hans Dieter Hüllstrung.

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Bürgi, U., Mendez, A., Hasler, P. et al. Hemophagocytic syndrome in adult-onset Still’s disease (AOSD): A must for biologics?—Case report and brief review of the literature. Rheumatol Int 32, 3269–3272 (2012). https://doi.org/10.1007/s00296-010-1497-z

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  • DOI: https://doi.org/10.1007/s00296-010-1497-z

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