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Catastrophic antiphospholipid syndrome presented with severe hypertension, adult respiratory distress syndrome and unilateral adrenal haemorrhagic infarction

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Abstract

We are reporting a case of catastrophic antiphospholipid syndrome (CAPS) in an adult female manifested with severe hypertension followed by adrenal haemorrhagic infarction and adult respiratory distress syndrome. Adrenal involvement appears to be exceedingly high in CAPS and adult respiratory distress syndrome (ARDS) is the prevailing pulmonary manifestation in this condition, compared with these impediments in patients with simple antiphospholipid syndrome (APS). Even though the above manifestations are well recognized, their combination as an initial presentation of CAPS is uncommon.

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Authors and Affiliations

  1. Department of Internal Medicine, Patras University Hospital, 26500, Rion, Patras, Greece

    Ioannis Starakis, Dimitris Siagris & Chrysoula Karatza

  2. Department of Internal Medicine, University General Hospital of Heraklion Crete, Crete, Greece

    Elias Mazokopakis

  3. Department of Rheumatology, Patras University Hospital, 26500, Rion, Patras, Greece

    Stamatis Liossis & Andrew Antonopoulos

Authors
  1. Ioannis Starakis
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  2. Elias Mazokopakis
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  3. Dimitris Siagris
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  4. Stamatis Liossis
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  5. Chrysoula Karatza
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  6. Andrew Antonopoulos
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Correspondence to Ioannis Starakis.

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Starakis, I., Mazokopakis, E., Siagris, D. et al. Catastrophic antiphospholipid syndrome presented with severe hypertension, adult respiratory distress syndrome and unilateral adrenal haemorrhagic infarction. Rheumatol Int 27, 781–783 (2007). https://doi.org/10.1007/s00296-007-0348-z

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  • DOI: https://doi.org/10.1007/s00296-007-0348-z

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