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Rheumatology International

, Volume 25, Issue 3, pp 234–237 | Cite as

Successful treatment with stent angioplasty for Budd-Chiari syndrome in Behçet’s disease

  • Seung Woo Han
  • Gun Woo Kim
  • Jongmin Lee
  • Yong Joo Kim
  • Young Mo KangEmail author
Case Report

Abstract

Budd-Chiari syndrome (BCS) is a very rare vascular complication of Behçet’s disease (BD) which often leads to death as a result of portal hypertension and liver failure. We report a 45-year-old BD patient who presented with BCS. Diagnosis was confirmed with CT scan and contrast-enhanced MR angiography which showed ascites, short-segment stenosis of the inferior vena cava (IVC), and middle and left hepatic venous thrombosis. Percutaneous transluminal angioplasty (PTA) of the obstructed segment in the IVC was performed and resulted in dramatic reduction of portal venous pressure. Our experience indicates that PTA may be a safe and effective therapeutic modality for BCS in BD which is caused by short segmental obstruction of the IVC.

Keywords

Behçet’s disease Budd-Chiari syndrome Percutaneous transluminal angioplasty 

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Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  • Seung Woo Han
    • 1
  • Gun Woo Kim
    • 1
  • Jongmin Lee
    • 2
  • Yong Joo Kim
    • 2
  • Young Mo Kang
    • 1
    Email author
  1. 1.Division of Rheumatology, Department of Internal MedicineKyungpook National University School of MedicineJunggu700–721 Republic of Korea
  2. 2.Department of Diagnostic RadiologyKyungpook National University School of MedicineJungguRepublic of Korea

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