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Leiomyosarkom der Vena cava inferior

Übersicht zu einem seltenen Krankheitsbild

Leiomyosarcoma of the inferior vena cava

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Zusammenfassung

Die sehr seltenen primären Leiomyosarkome der großen Gefäße sind am häufigsten in der Wandung der unteren Hohlvene entwickelt. Wir berichten über ein in toto resezierbares primäres, Progesteron-positives Leiomyosarkom am Übergang vom mittleren zum unteren V.-cava-inferior-Segment unterhalb des Abgangs der rechten V. renalis bei einer 41-jährigen Patientin. Wir gehen auf die derzeit bekannten Daten zu dem bisher mit knapp 300 Fallbeschreibungen publizierten Krankheitsbild ein.

Abstract

Primary sarcomas of the great vessels are rare. Their most common site is the inferior vena cava. We report a primary leiomyosarcoma of a 41 year old femal patient localised just below the right renal vein. The resected tumour showed the histological signs of a well differentiated, progesterone positive leiomyosarcoma. The case is discussed on the data of the reviewed literature.

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Danksagung

Die Autoren danken Herrn Prof. Dr. med. Katenkamp, Jena, für die Bestätigung der Diagnose.

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Der korrespondierende Autor versichert, dass keine Verbindungen mit einer Firma, deren Produkt in dem Artikel genannt ist, oder einer Firma, die ein Konkurrenzprodukt vertreibt, bestehen.

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Authors and Affiliations

  1. Institut für Pathologie der Ruhr-Universität Bochum an den Berufgenossenschaftlichen Kliniken Bergmannsheil

    A. M. Müller & K.-M. Müller

  2. Chirurgische Klinik der Universitätsklinik St. Josef-Hospital, Bochum

    A. M. Chromik, B. Bolik & U. Mittelkötter

  3. Institut für Pathologie der Ruhr-Universität an den Berufsgenossenschaftlichen Kliniken Bergmannsheil, Bürkle-de-la-Camp-Platz 1, 44789, Bochum

    A. M. Müller

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  1. A. M. Müller
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  2. A. M. Chromik
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  3. B. Bolik
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  4. K.-M. Müller
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  5. U. Mittelkötter
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Correspondence to A. M. Müller.

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Müller, A.M., Chromik, A.M., Bolik, B. et al. Leiomyosarkom der Vena cava inferior. Pathologe 26, 153–158 (2005). https://doi.org/10.1007/s00292-004-0745-y

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  • DOI: https://doi.org/10.1007/s00292-004-0745-y

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