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Mesenchymale Tumoren des Pankreas

Überraschend, aber nicht ungewöhnlich

Mesenchymal tumors of the pancreas

Surprising, but not uncommon

Zusammenfassung

Primäre mesenchymale Tumoren des Pankreas sind selten. Sie werden unter der Verdachtsdiagnose eines primären soliden oder zystischen Pankreastumors exploriert. Benigne mesenchymale Tumoren umfassen Lymphangiome, Hämangiome, Schwannome, solitäre fibröse Tumoren, Adenomatoidtumoren, den Klarzelltumor und Hamartome. Eine Sonderstellung nehmen die inflammatorischen Pseudotumoren ein. Unter den malignen mesenchymalen Tumoren finden sich Leiomyosarkome, maligne periphere Nervenscheidentumoren (MPNST), Liposarkome, maligne fibröse Histiozytome, Ewing-Sarkome und primitive neuroektodermale Tumoren (PNET). Wichtig ist die differenzialdiagnostische Abgrenzung gegenüber anaplastischen Karzinomen und retroperitonealen mesenchymalen Tumoren mit Infiltration in das Pankreas.

Abstract

Mesenchymal tumors of the pancreas are rare. They are resected because a solid or cystic pancreatic tumor is suspected. Benign mesenchymal tumors comprise lymphangiomas, hemangiomas, schwannomas, solitary fibrous tumors, adenomatoid tumors, clear cell tumors, and hamartomas. Inflammatory pseudotumors are a special case. Malignant mesenchymal tumors include leiomyosarcomas, malignant peripheral nerve sheath tumors (MPNST), liposarcomas, malignant fibrous histiocytomas, Ewing’s sarcomas, and primitive neuroectodermal tumors (PNET). It is important to differentiate these tumors from anaplastic carcinomas and retroperitoneal tumors that infiltrate pancreatic tissue.

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Pauser, U., Kosmahl, M., Sipos, B. et al. Mesenchymale Tumoren des Pankreas. Pathologe 26, 52–58 (2005). https://doi.org/10.1007/s00292-004-0730-5

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Schlüsselwörter

  • Mesenchymale Tumoren
  • Solitär fibröser Tumor
  • Zystischer Pankreastumors
  • Inflammatorischer Pseudotumor
  • Immunhistochemie

Keywords

  • Soft tissue tumors
  • Solitary fibrous tumor
  • Cystic pancreatic tumor
  • Inflammatory pseudotumor
  • Immunohistochemistry