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Immunological diseases of the pancreatico-hepatobiliary system: update on etiopathogenesis and cross-sectional imaging findings

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Abstract

Immunological diseases of the hepatobiliary system and the pancreas include a broad spectrum of disorders that manifest characteristic histopathology/serology and variable clinical features and imaging findings. Recent studies have thrown fresh light on the complex role of genetics and autoimmunity in the pathogenesis and natural history of these diverse disorders that include autoimmune hepatitis, primary biliary cirrhosis, primary sclerosing cholangitis, IgG4-related cholangitis, overlap/outlier syndromes, and autoimmune pancreatitis.

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Authors and Affiliations

  1. Department of Radiology, University of Texas Health Science Center, San Antonio, TX, 78229, USA

    Deepak Garg, Shaile Philips & Alampady K. Shanbhogue

  2. Department of Radiology, Ohio State University Medical Center, 395 W 12th Ave, Columbus, OH, 43210, USA

    Arpit Nagar

  3. Department of Radiology, Mayo Clinic, 200 First Street S.W., Rochester, MN, 55905, USA

    Naoki Takahashi

  4. Department of Radiology, University of Texas MD Anderson Cancer Center, 1400 Pressler Street, Houston, TX, 77030, USA

    Srinivasa R. Prasad

  5. Department of Radiology, Massachusetts General Hospital, 55 Fruit Street, Boston, MA, 02114, USA

    Dushyant V. Sahani

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  1. Deepak Garg
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  2. Arpit Nagar
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  3. Shaile Philips
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  4. Naoki Takahashi
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  6. Alampady K. Shanbhogue
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Correspondence to Srinivasa R. Prasad.

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Garg, D., Nagar, A., Philips, S. et al. Immunological diseases of the pancreatico-hepatobiliary system: update on etiopathogenesis and cross-sectional imaging findings. Abdom Imaging 37, 261–274 (2012). https://doi.org/10.1007/s00261-011-9759-0

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