Abstract
Endogenous Cushing’s syndrome is a relatively rare disease. Most cases being ACTH-dependent, ACTH-independent Cushing’s syndrome (AICS) is an even rarer condition [15%–20%]. In more than 95% cases the cause of AICS is unilateral adrenal enlargement caused by adenoma or carcinoma. Bilateral adrenal disease is caused by primary pigmented nodular adrenal dysplasia (PPNAD) and ACTH-independent macro nodular hyperplasia (AIMAH). Only few case reports of the latter condition exist in the radiology literature, PPNAD being the commoner of two as the cause for AICS.
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Verma, A., Mohan, S. & Gupta, A. ACTH-independant macronodular adrenal hyperplasia: imaging findings of a rare condition. Abdom Imaging 33, 225–229 (2008). https://doi.org/10.1007/s00261-007-9236-y
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DOI: https://doi.org/10.1007/s00261-007-9236-y