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Update of pediatric bone tumors—notochordal tumors, chondrogenic tumors, and vascular tumors of the bone

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Abstract

There are numerous bone tumors in the pediatric population, with imaging playing an essential role in diagnosis and management. Our understanding of certain bone tumors has rapidly evolved over the past decade with advancements in next-generation genetic sequencing techniques. This increased level of understanding has altered the nomenclature, management approach, and prognosis of certain lesions. We provide a detailed update of bone tumors that occur in the pediatric population with emphasis on the recently released nomenclature provided in the 5th edition of the World Health Organization Classification of Soft Tissue and Bone Tumours. In the current manuscript, we address notochordal tumors, chondrogenic tumors, and vascular tumors of the bone.

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Correspondence to Jack Porrino.

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Lee, H., Wang, A., Cheng, R. et al. Update of pediatric bone tumors—notochordal tumors, chondrogenic tumors, and vascular tumors of the bone. Skeletal Radiol 52, 1101–1117 (2023). https://doi.org/10.1007/s00256-022-04235-x

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