Skeletal Radiology

, Volume 47, Issue 4, pp 579–585 | Cite as

Parosteal extra-axial chordoma of the second metacarpal bone: a case report with literature review

  • Shinji Tsukamoto
  • Daniel Vanel
  • Alberto Righi
  • Davide Maria Donati
  • Costantino Errani
Case Report


Extra-axial chordoma is a chordoma that occurs in non-axial locations. It is a very rare tumor, with 20 cases reported to date; 14 in bone and six in soft tissue. Of the 14 skeletal extra-axial chordomas, ten were intramedullary and four were intracortical. We report the first case of parosteal extra-axial chordoma arising in the second metacarpal bone, expressing brachyury on immunohistochemical analysis, and describe the pathologic and radiologic findings. We suggest that extra-axial chordoma can occur in parosteal bone lesions or the hand, without features of bone distribution or bone-specific sites.


Chordoma Parachordoma Extra-axial chordoma Brachyury Metacarpal bone Parosteal 


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflicts of interest.

Author statement

All authors had access to data and a role in writing the manuscript.


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Copyright information

© ISS 2017

Authors and Affiliations

  • Shinji Tsukamoto
    • 1
  • Daniel Vanel
    • 2
  • Alberto Righi
    • 2
  • Davide Maria Donati
    • 1
  • Costantino Errani
    • 1
  1. 1.Department of Orthopaedic OncologyRizzoli InstituteBolognaItaly
  2. 2.Department of PathologyRizzoli InstituteBolognaItaly

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