Abstract
Chordomas are rare, slow-growing tumors arising from cellular remnants of the notochord. They account for 1–4 % of primary malignant bone tumors and usually occur in the axial skeleton, most commonly the sacrum. Although typically locally recurrent, chordoma metastasis rates as high as 10–42 % have been reported. While spread to multiple organ systems has been documented, metastatic disease to skeletal muscle is extremely rare. We present a case of extensive, multifocal skeletal muscle metastases developing in the setting of recurrent sacral chordoma. Our literature search found only one additional case of metastatic chordoma to a single skeletal muscle.
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Acknowledgments
The authors would like to thank Dr. Jon Dalton, MD, for his assistance with the preparation and review of this manuscript. The authors would also like to thank Kelly Viola, ELS, for her editorial assistance.
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Carey, K., Bestic, J., Attia, S. et al. Diffuse skeletal muscle metastases from sacral chordoma. Skeletal Radiol 43, 985–989 (2014). https://doi.org/10.1007/s00256-013-1794-1
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DOI: https://doi.org/10.1007/s00256-013-1794-1