Abstract
We report here the imaging findings of a rare case of a lethal form of Gorham disease in a young female patient. Multimodality imaging findings over 13 year-follow-up demonstrated progressive wide spread skeletal and soft tissue abnormalities with permeative osteolysis, pathological fractures and severe skeletal deformities. Unusual extensive osseous and soft tissue pneumatosis was illustrated on cross-sectional studies. The progressive nature of this form of Gorham disease and the subsequent complications eventually culminated in patient’s death.
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Atalabi, O.M., Fishman, S.J., Kozakewich, H.P. et al. A lethal form of Gorham disease associated with extensive musculoskeletal pneumatosis: case report and review of the literature. Skeletal Radiol 37, 1041–1046 (2008). https://doi.org/10.1007/s00256-008-0525-5
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DOI: https://doi.org/10.1007/s00256-008-0525-5