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Multifocal PVNS in a child – followed over 25 years

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Abstract

Pigmented villonodular synovitis (PVNS) is a rare disorder of unknown aetiology, characterised by a destructive fibrohistiocytic proliferation with production of villous and nodular protrusions. The disease is commonly monoarticular, and involves the knee in 80% of cases. Occurrence in a child and involvement of multiple joints are extremely unusual. We present a case of multiple joint PVNS in a patient who first presented at the age of five and was subsequently followed up for over twenty-five years. The literature on the subject is briefly reviewed.

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Authors and Affiliations

  1. Derriford Hospital Radiology, Plymouth, UK

    Kausik Mukhopadhyay & P. M. Hughes

  2. Derriford Hospital Histopathology, Plymouth, UK

    M. Smith

  3. 14 Lister Close, Exeter, EX2 4SD, UK

    Kausik Mukhopadhyay

Authors
  1. Kausik Mukhopadhyay
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  2. M. Smith
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  3. P. M. Hughes
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Correspondence to Kausik Mukhopadhyay.

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Mukhopadhyay, K., Smith, M. & Hughes, P.M. Multifocal PVNS in a child – followed over 25 years. Skeletal Radiol 35, 539–542 (2006). https://doi.org/10.1007/s00256-005-0013-0

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  • DOI: https://doi.org/10.1007/s00256-005-0013-0

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