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Primary clear cell sarcoma of rib

Skeletal Radiology volume 34, pages 167–170 (2005)Cite this article

Abstract

Clear cell sarcoma (malignant melanoma of soft tissues) is a very rare soft tissue neoplasm. It generally arises in tendons and aponeuroses. Although metastasis of malignant melanoma to bone is not uncommon, primary clear cell sarcoma of bone is an extremely rare neoplasm. To our knowledge five cases have been reported in the English literature. We present a case of primary clear cell sarcoma of bone in a 28-year-old woman arising in the left ninth rib. We treated the patient with total excision of the mass and postoperative radiotherapy. The patient is alive and well without local recurrence or distant metastasis at 33 months after surgery.

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Acknowledgement

Cytogenetic analysis of the patient was carried out by Prof. Dr. P.C.W. Hogendoorn, Leiden, The Netherlands. We thank him for his kind help and assistance.

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Affiliations

  1. Department of Orthopedics and Traumatology, Baskent University Medical Faculty, Adana, Turkey

    Murat Ali Hersekli, Gurkan Ozkoc, Sercan Akpinar, Metin Ozalay & Reha N. Tandogan

  2. Adana Medical Center, Baskent University Medical Faculty, Dadaloglu mah. 39. sok No:6, 01250, Yuregir Adana, Turkey

    Murat Ali Hersekli

  3. Department of Pathology, Suleyman Demirel University Medical Faculty, Adana, Turkey

    Sema Bircan

  4. Department of Pathology, Baskent University Medical Faculty, Adana, Turkey

    Ilhan Tuncer

Authors
  1. Murat Ali Hersekli
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  2. Gurkan Ozkoc
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  3. Sema Bircan
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  4. Sercan Akpinar
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  5. Metin Ozalay
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  6. Ilhan Tuncer
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  7. Reha N. Tandogan
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Corresponding author

Correspondence to Murat Ali Hersekli.

Additional information

Presented at SICOT/SIROT 2002 XXII World Congress, San Diego, California, USA, August 23–30, 2002

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Hersekli, M.A., Ozkoc, G., Bircan, S. et al. Primary clear cell sarcoma of rib. Skeletal Radiol 34, 167–170 (2005). https://doi.org/10.1007/s00256-004-0801-y

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  • DOI: https://doi.org/10.1007/s00256-004-0801-y

Keywords

  • Rib
  • Primary
  • Clear cell sarcoma
  • Malignant melanoma of soft parts
  • CT