Congenital subependymal giant-cell astrocytoma: case report with prenatal ultrasonogram

Abstract

Background. A prenatal sonogram at 27 weeks of gestation revealed a brain mass along the frontal horn and body of the lateral ventricle near the foramen of Monro in the fetus. Materials and methods. A huge subependymal giant-cell astrocytoma was nearly totally resected at 11 days of age. Results. There was no syndromic family history, but features substantiating the diagnosis of tuberous sclerosis were recognized at 4 years of age. Conclusion. The sonographic finding of a tumor in the region of the foramen of Monro should raise the suspicion of a subependymal giant-cell astrocytoma, a tumor characteristically associated with tuberous sclerosis.