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Overview of the clinical and imaging features of the most common non-rhabdomyosarcoma soft-tissue sarcomas

Abstract

Non-rhabdomyosarcoma soft-tissue sarcoma (NRSTS) refers to a widely heterogeneous group of extraskeletal mesenchymal neoplasms accounting for approximately 4% of all childhood cancers. This article summarizes the clinical and imaging features of these rare tumors and describes in detail the three most common histological types of NRSTSs encountered in children — synovial sarcoma, malignant peripheral nerve sheath tumor and infantile fibrosarcoma. The author discusses the role of non-cross-sectional and cross-sectional imaging.

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Correspondence to Simon C. Kao.

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Kao, S.C. Overview of the clinical and imaging features of the most common non-rhabdomyosarcoma soft-tissue sarcomas. Pediatr Radiol 49, 1524–1533 (2019). https://doi.org/10.1007/s00247-019-04427-z

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Keywords

  • Children
  • Computed tomography
  • Magnetic resonance imaging
  • Non-rhabdomyosarcoma soft-tissue sarcoma
  • Oncology
  • Positron emission tomography
  • Ultrasound