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Overview of the clinical and imaging features of the most common non-rhabdomyosarcoma soft-tissue sarcomas

Pediatric Radiology volume 49, pages 1524–1533 (2019)Cite this article

Abstract

Non-rhabdomyosarcoma soft-tissue sarcoma (NRSTS) refers to a widely heterogeneous group of extraskeletal mesenchymal neoplasms accounting for approximately 4% of all childhood cancers. This article summarizes the clinical and imaging features of these rare tumors and describes in detail the three most common histological types of NRSTSs encountered in children — synovial sarcoma, malignant peripheral nerve sheath tumor and infantile fibrosarcoma. The author discusses the role of non-cross-sectional and cross-sectional imaging.

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Authors and Affiliations

  1. Department of Radiology,, University of Iowa Carver College of Medicine,, 200 Hawkins Drive, 3885JPP, Iowa City, IA, 52242, USA

    Simon C. Kao

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  1. Simon C. Kao
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Correspondence to Simon C. Kao.

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Kao, S.C. Overview of the clinical and imaging features of the most common non-rhabdomyosarcoma soft-tissue sarcomas. Pediatr Radiol 49, 1524–1533 (2019). https://doi.org/10.1007/s00247-019-04427-z

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  • DOI: https://doi.org/10.1007/s00247-019-04427-z

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