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Pediatric Radiology

, Volume 46, Issue 3, pp 422–425 | Cite as

Development of bilateral coronary artery aneurysms in a child with Noonan syndrome

  • David M. Mauro
  • Lucia Flors
  • Andrew W. Hoyer
  • Patrick T. Norton
  • Klaus D. HagspielEmail author
Case Report

Abstract

Noonan syndrome is a constellation of congenital malformations including heart defects, facial anomalies and short stature. The cardiovascular defects are variable and extensive, with the most common being pulmonary stenosis and hypertrophic cardiomyopathy. Coronary artery anomalies have only been reported in a few cases. We report a child with Noonan syndrome status post pulmonary stenosis and atrial septal defect repair, who developed bilateral coronary artery aneurysms. The aneurysms were diagnosed with both cardiac magnetic resonance imaging and coronary computed tomography angiography. There had been no evidence of them on a cardiac MR exam 5 years previously.

Keywords

Child Computed tomography Coronary aneurysm Coronary artery Magnetic resonance imaging Noonan syndrome 

Notes

Acknowledgments

K.D.H. and P.T.N. receive grant support from Siemens Medical Solutions, Malvern, PA, USA.

Compliance with Ethical Standards

Conflicts of interest

None

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Copyright information

© Springer-Verlag Berlin Heidelberg 2015

Authors and Affiliations

  • David M. Mauro
    • 1
  • Lucia Flors
    • 1
  • Andrew W. Hoyer
    • 2
    • 3
  • Patrick T. Norton
    • 1
  • Klaus D. Hagspiel
    • 1
    Email author
  1. 1.Department of Radiology and Medical ImagingUniversity of Virginia Health SystemCharlottesvilleUSA
  2. 2.Department of Pediatrics, Division of Pediatric CardiologyUniversity of Virginia Health SystemCharlottesvilleUSA
  3. 3.Pediatric Cardiology Center of OregonPortlandUSA

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