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Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum

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Abstract

We report the case of a newborn with pulmonary atresia with intact ventricular septum and right ventricle-dependent coronary circulation. He died several weeks after a Blalock-Taussig procedure because of a progressive stenosis of the main coronary artery. We present echocardiographic and dual-source CT images of the stenosis, with autopsy correlation. To our knowledge, CT images of this quality have never been reported in a newborn. This case illustrates the extreme difficulty in prognosticating the outcome for these patients and underlines the need for a detailed neonatal coronary mapping to assess right ventricle-dependent coronary circulation.

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Authors and Affiliations

  1. Department of Pediatric Cardiology, Centre Chirurgical Marie Lannelongue, Le Plessis-Robinson, France

    Pierre-Emmanuel Séguéla, Lucile Houyel & Jean-Dominique Piot

  2. Department of Pathology, Centre Hospitalier Universitaire de Rennes, Rennes, France

    Philippe Loget

  3. Department of Pediatric Radiology, Centre Chirurgical Marie Lannelongue, Le Plessis-Robinson, France

    Jean-François Paul

  4. Hôpital des Enfants, 330 Avenue de Grande-Bretagne, TSA 70034, 31059, Toulouse Cedex 9, France

    Pierre-Emmanuel Séguéla

Authors
  1. Pierre-Emmanuel Séguéla
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  2. Lucile Houyel
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  3. Philippe Loget
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  4. Jean-Dominique Piot
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  5. Jean-François Paul
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Correspondence to Pierre-Emmanuel Séguéla.

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Séguéla, PE., Houyel, L., Loget, P. et al. Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum. Pediatr Radiol 41, 1069–1072 (2011). https://doi.org/10.1007/s00247-011-2068-5

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  • DOI: https://doi.org/10.1007/s00247-011-2068-5

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