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Ectopia cordis with tetralogy of Fallot in an infant with pentalogy of Cantrell: high-pitch MDCT exam

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We report the MDCT findings of a 17-month-old girl with Cantrell´s pentalogy, a rare congenital disease characterized by several defects in the ventral thoracoabdominal wall including ectopia cordis, and, in this patient, associated with tetralogy of Fallot. This case provides an example of the utility of a wide volume in coverage and high-pitch MDCT scan in the evaluation of complex cardiovascular anatomy in infants with congenital heart disease without the need of an ECG-gating acquisition.

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  1. Van Hoorn JH, Moonen RM, Huysentruyt CJ et al (2008) Pentalogy of Cantrell: two patients and a review to determine prognostic factors for optimal approach. Eur J Pediatr 167:29–35

    Article  PubMed  Google Scholar 

  2. Carmi R, Boughman JA (1992) Pentalogy of Cantrell and associated midline anomalies: a possible ventral midline developmental field. Am J Med Genet 42:90–95

    Article  PubMed  CAS  Google Scholar 

  3. Toyama WM (1972) Combined congenital defects of the anterior abdominal wall, sternum, diaphragm, pericardium, and heart: a case report and review of the syndrome. Pediatrics 50:778–792

    PubMed  CAS  Google Scholar 

  4. Brooks M, Zietman A (1998) Clinical embryology: a color atlas and text. CRC Press, Boca Raton, FL

    Google Scholar 

  5. Vasquez-Jimenez JF, Muehler EG, Daebritz S et al (1998) Cantrell’s syndrome: a challenge to the surgeon. Ann Thorac Surg 65:1178–1185

    Article  Google Scholar 

  6. Lell M, Marwan M, Schepis T et al (2009) Prospectively ECG-triggered high-pitch spiral acquisition for coronary CT angiography using dual source CT: technique and initial experience. Eur Radiol 19:2576–2583

    Article  PubMed  Google Scholar 

  7. Leipsic J, LaBounty TM, Heilbron B et al (2010) Estimated radition dose reduction using adaptive statistical iterative reconstruction in coronary CT angiography: the ERASIR study. AJR 195:655–660

    Article  PubMed  Google Scholar 

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Correspondence to Eric Kimura-Hayama.

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Santiago-Herrera, R., Ramirez-Carmona, R., Criales-Vera, S. et al. Ectopia cordis with tetralogy of Fallot in an infant with pentalogy of Cantrell: high-pitch MDCT exam. Pediatr Radiol 41, 925–929 (2011).

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