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POEMS syndrome in a 15-year-old boy: radiological findings

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Abstract

POEMS syndrome is a multisystem disorder related to a plasma-cell dyscrasia. It is usually seen between the ages of 40 and 50 years and is very rare in childhood. Radiologically, this syndrome is characterized by sclerotic focal bone lesions with a normal radionuclide bone scan. We report a case of POEMS syndrome in a 15-year-old boy in whom plain radiographs and multidetector-row spiral CT (MDCT) provided information that was helpful in the clinical assessment.

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Authors and Affiliations

  1. Paediatric Radiology Department, Azienda Ospedaliero-Universitaria Ospedali Riuniti, via Corridoni 11, Ancona, 60123, Italy

    Cecilia Lanza & Giancarlo Fabrizzi

  2. University Department of Radiology, Azienda Ospedaliero-Universitaria Ospedali Riuniti, Ancona, Italy

    Marco Misericordia

Authors
  1. Cecilia Lanza
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  2. Marco Misericordia
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  3. Giancarlo Fabrizzi
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Correspondence to Cecilia Lanza.

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Lanza, C., Misericordia, M. & Fabrizzi, G. POEMS syndrome in a 15-year-old boy: radiological findings. Pediatr Radiol 37, 1147–1150 (2007). https://doi.org/10.1007/s00247-007-0561-7

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  • DOI: https://doi.org/10.1007/s00247-007-0561-7

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