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MRI diagnosis of isolated origin of the left subclavian artery from the left pulmonary artery

Pediatric Radiology volume 35, pages 1259–1262 (2005)Cite this article

Abstract

Right aortic arch with isolation of the left subclavian artery is a rare disorder. In this entity, the left subclavian artery has its origin from the pulmonary artery via the ductus arteriosus. We report an infant with an unbalanced atrioventricular septal defect, right aortic arch, bilateral ductus arteriosi and an isolated left subclavian artery. This infant also had chromosome 22q11 deletion. The origin and course of the isolated subclavian artery were well-demonstrated using contrast-enhanced 3-D magnetic resonance angiography. This non-invasive diagnostic modality can accurately reveal detailed mediastinal vascular anatomy in a young infant and allows diagnosis of aberrant vascular connections.

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Affiliations

  1. Department of Diagnostic Imaging, The Hospital for Sick Children, University of Toronto, 555 University Ave., M5G 1X8, Toronto, ON, Canada

    Ai-Min Sun, Helen Branson & Shi-Joon Yoo

  2. Department of Pediatrics, Division of Cardiology, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada

    Fahad Alhabshan & Robert M. Freedom

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  1. Ai-Min Sun
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  2. Fahad Alhabshan
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  3. Helen Branson
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  4. Robert M. Freedom
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  5. Shi-Joon Yoo
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Correspondence to Shi-Joon Yoo.

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Sun, AM., Alhabshan, F., Branson, H. et al. MRI diagnosis of isolated origin of the left subclavian artery from the left pulmonary artery. Pediatr Radiol 35, 1259–1262 (2005). https://doi.org/10.1007/s00247-005-1569-5

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  • DOI: https://doi.org/10.1007/s00247-005-1569-5

Keywords

  • MR angiography
  • Right aortic arch
  • Subclavian artery
  • Bilateral patent ductus arteriosi
  • 22q11 deletion