Abstract
Congenital lobar emphysema (CLE) is a cause of severe neonatal respiratory distress. Overexpansion of the affected pulmonary lobe in the fetus is due to narrowing of the airway, with a resultant ‘ball-valve’ effect. At birth, there may be delayed clearance of fetal lung fluid. Early chest radiographs show opacification of the hyperexpanded lobe. The CT findings in the immediate neonatal period have not been previously reported. We describe the imaging in a neonate with tetralogy of Fallot and absent pulmonary valve with secondary CLE. CT demonstrates the hyperexpanded lobe with initial thickening of the interlobular septa and alveolar ground glass attenuation, with subsequent clearing. This resorption of fetal lung fluid via the pulmonary interstitium should not be confused with interstitial lung disease.
Similar content being viewed by others
References
Borg SA, Young LW, Roghair GD (1975) Congenital avalvular pulmonary artery and infantile lobar emphysema: a diagnostic correlation. Am J Roentgenol Radium Ther Nucl Med 125:412–421
Stigers KB, Woodring JH, Kanga JF (1992) The clinical and imaging spectrum of findings in patients with congenital lobar emphysema. Pediatr Pulmonol 14:160–170
Strife JL, Towbin RB, Francis P, et al (1981) Retained fetal lung fluid in two neonates with congenital absence of the pulmonary valve and tetralogy of Fallot. Radiology 141:675–677
Madan A, Parisi M, Wood B (1992) Radiological case of the month: absent pulmonary valve presenting with congenital lobar emphysema. Am J Dis Child 146:113–114
Newman B, Kuhn JP, Kramer SS, et al (2001) Congenital surfactant protein B deficiency—emphasis on imaging. Pediatr Radiol 31:327–331
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Fink, A.M., Edis, B. & Massie, J. The CT appearances of delayed amniotic fluid clearance from the lungs in an infant with absent pulmonary valve and congenital lobar emphysema. Pediatr Radiol 35, 891–894 (2005). https://doi.org/10.1007/s00247-005-1469-8
Received:
Revised:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00247-005-1469-8