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Chiari Network Associated with Hypoxemia in a Neonate: Case Report and Review of the Literature

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Abstract

Chiari network is an embryonic remnant of the right sinus venosus. It appears as a thin, fenestrated membrane attached to two or more regions within the right atrium. Usually, a Chiari network has a benign course; however, rare complications associated with a Chiari network have been reported. We present the case of a neonate with hypoxemia and a Chiari network protruding into the right ventricular inflow tract associated with right-to-left shunting across the patent foramen ovale throughout the cardiac cycle. We noted spontaneous improvement after 3 weeks of life.

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Funding

The authors declare that they have no funding support for this case report.

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Authors and Affiliations

  1. Section of Pediatric Cardiology, Department of Pediatrics, Rush University Medical Center, Chicago, IL, USA

    Saif Aljemmali, John Bokowski & Raymond Morales

  2. Division of Cardiology, Ann & Robert H. Lurie Children’s Hospital of Chicago; Department of Pediatrics, Northwestern University Feinberg School of Medicine, Chicago, IL, USA

    Ra-id Abdulla

Authors
  1. Saif Aljemmali
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  2. John Bokowski
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  3. Raymond Morales
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  4. Ra-id Abdulla
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Correspondence to Saif Aljemmali.

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Supplementary file1—Subcostal long and short-axis views of echocardiography. Chiari Network is demonstrated in the right atrium protruding into the right ventricle through the tricuspid valve (AVI 53103 kb)

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Aljemmali, S., Bokowski, J., Morales, R. et al. Chiari Network Associated with Hypoxemia in a Neonate: Case Report and Review of the Literature. Pediatr Cardiol 41, 1529–1531 (2020). https://doi.org/10.1007/s00246-020-02432-w

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  • DOI: https://doi.org/10.1007/s00246-020-02432-w

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