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Two Cases of a Prenatally Diagnosed Double Aortic Arch with Postnatal Obliteration of the Distal Left Aortic Arch

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Abstract

We report two cases of prenatally diagnosed double aortic arch with dominant right arch and a left-sided ductus arteriosus, consistent with a complete vascular ring. Postnatal transthoracic echocardiogram and cardiac magnetic resonance imaging demonstrated a spontaneous closure of the ductus arteriosus and obliteration of the left aortic arch distal to the origin of the left subclavian artery in both cases. Spontaneous closure of the ductus arteriosus involving extended ductal tissue in the left aortic arch likely led to obliteration of the distal left arch after birth. One patient presented with recurrent symptoms suggestive of dysphagia and underwent a successful surgical repair of the vascular ring with resolution of symptoms. The other patient has been asymptomatic and is 4 years old at the time of this report.

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Authors and Affiliations

  1. The Lillie Frank Abercrombie Section of Cardiology, Department of Pediatrics, Texas Children’s Hospital, Baylor College of Medicine, 6651 Main Street. Legacy Tower, E1920, Houston, TX, 77030-2303, USA

    Tam T. Doan

  2. Department of Pediatric Cardiology, Connecticut Children’s Medical Center and University of Connecticut School of Medicine, Hartford, CT, 06106, USA

    Alicia Wang, Brooke Davey, Shailendra Upadhyay & Olga Toro-Salazar

Authors
  1. Tam T. Doan
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  2. Alicia Wang
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  3. Brooke Davey
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  4. Shailendra Upadhyay
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  5. Olga Toro-Salazar
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Corresponding author

Correspondence to Tam T. Doan.

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This study has no financial aid. Authors declare that there is no conflict of interest.

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All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

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Informed consent was not obtained for this case report.

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The cases were reported from Connecticut Children’s Medical Center, 282 Washington Street, Hartford, CT 06106, USA

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Doan, T.T., Wang, A., Davey, B. et al. Two Cases of a Prenatally Diagnosed Double Aortic Arch with Postnatal Obliteration of the Distal Left Aortic Arch. Pediatr Cardiol 40, 1748–1751 (2019). https://doi.org/10.1007/s00246-019-02141-z

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  • DOI: https://doi.org/10.1007/s00246-019-02141-z

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