Pediatric Cardiology

, Volume 39, Issue 4, pp 824–828 | Cite as

Large Calibre Self-Expanding Stents for Pulmonary Stenosis After the Arterial Switch, a Low-Risk Solution to a Low-Flow Situation

  • Gareth J. Morgan
  • Kuberan Pushparajah
  • Srinivas Narayan
  • Eric Rosenthal
Original Article


Branch pulmonary artery stenosis is one of the most common complications late after the arterial switch operation. The pathophysiology of stenosis in these circumstances is very different to that encountered in with normally related great vessels. The LeCompte manoeuvre leaves the pulmonary arteries straddled and stretched over the aortic root which contributing significantly to the degree of stenosis encountered. Unilateral branch pulmonary artery stenosis rarely leads to significant symptoms in young patients with biventricular repairs; however, significant discrepancies in the split flows between right and left lung may place the patient in an unfavourable physiological position as they move in to middle age. Balloon expandable stent implantation distorts the anatomical arrangement of the LeCompte and is associated with negative interactions with the often dilated aortic root. We present three cases of the use of flexible self-expanding stents to improve the physiological flow distributions to each lung whilst hopefully decreasing the risk of erosion and perforation or fistula formation related to the pulmonary artery. All three patients had uncomplicated procedures with significant improvements in vessel diameter and flow distribution noted on follow-up MRI scans. This is the first report of the use of self-expanding stents in the context of branch pulmonary artery stenosis after the LeCompte manoeuvre. Theoretically and based on our early experience, this technique provides potential safety advantages over the use of more traditional balloon expandable stents.


LeCompte Pulmonary stenting Aorto-pulmonary fistula 


Compliance with Ethical Standards

Conflict of interest

None of the authors declare and conflict of interest.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Informed Consent

Informed consent was obtained from all individual participants included in the study.


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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2018

Authors and Affiliations

  • Gareth J. Morgan
    • 1
    • 2
    • 3
  • Kuberan Pushparajah
    • 2
    • 3
  • Srinivas Narayan
    • 2
    • 3
  • Eric Rosenthal
    • 2
    • 3
  1. 1.The Heart Institute, Childrens’ Hospital of ColoradoUniversity of Colorado, Anschutz Medical CampusDenverUSA
  2. 2.Evelina London Childrens HospitalLondonUK
  3. 3.Kings College LondonLondonUK

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