Pediatric Cardiology

, Volume 38, Issue 7, pp 1519–1521 | Cite as

Critically Underdeveloped Left Heart Morphology Associated with Prematurity and Low Birth Weight: Conditional Staged Rehabilitation Towards Biventricular Repair and Time-Related Growth of Left Heart Structures

  • Fareed Ahmad
  • Robert Mangano
  • Shirah Shore
  • Anastasios Polimenakos
Case Report

Abstract

This is a case report of premature low birth weight infant with hypoplasia of left heart structures and a large malaligned VSD who underwent successful staged approach of biventricular repair. We obtained qualitative and quantitative echocardiographic, MRI, and conventional catheterization data to support stepwise strategy towards LV rehabilitation to sustain adequate cardiac output. A thorough and intense follow-up has shown significant growth of left heart structures and favorable clinical status following staged biventricular repair. Our data indicate usefulness of qualitative and quantitative advanced complimentary multi-imaging modalities in predicting the postnatal growth potential of critically underdeveloped left heart structures.

Keywords

Hypoplastic left ventricle Volumetric analysis Congenital 

Notes

Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards.

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Copyright information

© Springer Science+Business Media New York 2017

Authors and Affiliations

  • Fareed Ahmad
    • 1
  • Robert Mangano
    • 1
  • Shirah Shore
    • 1
  • Anastasios Polimenakos
    • 1
  1. 1.Janet Weis Children hospitalGeisinger Health SystemDanvilleUSA

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